01 Primary sclerosing cholangitis as a first manifestation of hyper IgM syndrome
نویسندگان
چکیده
منابع مشابه
Recurrent Gallbladder Hydrops and Sclerosing Cholangitis in 11-Year-Old Male with Hyper IgM Syndrome
Hyper Immunoglobulin M (hyper IgM) is a rare immunodeficiency disorder first reported in 1961[1], characterized by recurrent infections with low levels of serum IgA, IgG and IgE and normal to high levels of serum IgM[1]. Onset of manifestation of X-linked HIGM occurs in the 1st or 2nd year of life with recurrent pyogenic infections especially of upper and lower respiratory tract and diarrhea in...
متن کاملImproving Symptoms of Primary Sclerosing Cholangitis by Iranian Traditional Medicine
Introduction: Primary Sclerosing Cholangitis (PSC) is a chronic cholestatic disease that results from the inflammation and destruction of intra- and extra-hepatic bile ducts and fibrosis which can lead to cirrhosis. The purpose of this report is to provide the clinical experience of Iranian traditional medicine with the best therapeutic effect within the shortest time. <s...
متن کاملPrimary sclerosing cholangitis as an intractable disease.
Primary sclerosing cholangitis (PSC) is a chronic cholestatic liver disease of unknown origin which eventually results in liver cirrhosis. The disease is reported to be more common among the Western population than in the Asian population. Asian experience remains limited. Diagnosis and treatment standards in the Far East have largely followed those in the West, including liver transplantation....
متن کاملPrimary sclerosing cholangitis
Primary sclerosing cholangitis (PSC) is a chronic inflammatory disorder of the biliary system that results in progressive fibrosis and strictures of the intrahepatic and extrahepatic bile ducts. Typical radiological changes on retrograde cholangiography are shown in Figure 1. These strictures cause cholestatic liver disease that may progress to end-stage cirrhosis. The disorder has a strong ass...
متن کاملPrimary Sclerosing Cholangitis: Introduction
The prevalence of primary sclerosing cholangitis in the United States is approximately 1–6 cases per 100,000 population. Most patients with primary sclerosing cholangitis are men (75%) with an average age of approximately 40 years at diagnosis. The overwhelming majority of patients affected with primary sclerosing cholangitis are Caucasian. The etiology is unknown but current opinion favors an ...
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ژورنال
عنوان ژورنال: International Journal of Infectious Diseases
سال: 2006
ISSN: 1201-9712
DOI: 10.1016/s1201-9712(06)80001-9